E71.110
✓ Billable
Isovaleric acidemia
ICD-10-CM · FY2026 · Endocrine, Nutritional and Metabolic Diseases
Code
E71.110
System
ICD-10-CM
Billable
Yes — valid for submission
Effective
FY2026
Chapter
Endocrine, Nutritional and Metabolic Diseases
Source
CMS / CDC NCHS
⚠ Verify before billing. Confirm against the current CMS/NCHS ICD-10-CM files and your payer's rules before claims submission.
Frequently asked questions
What is ICD-10 code E71.110?
ICD-10-CM code E71.110 represents Isovaleric acidemia. It is a billable diagnosis code in the Endocrine, Nutritional and Metabolic Diseases chapter, effective October 1, 2025 – September 30, 2026.
Is E71.110 billable?
Yes. E71.110 is a valid billable ICD-10-CM code for insurance claims and clinical documentation.
What chapter is E71.110 in?
E71.110 belongs to the Endocrine, Nutritional and Metabolic Diseases chapter (E00–E89) of ICD-10-CM.
Related codes in the E71 category
E71
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E71.0
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E71.1
Other disorders of branched-chain amino-acid metabolism
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E71.2
Disorder of branched-chain amino-acid metabolism, unspecified
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E71.3
Disorders of fatty-acid metabolism
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E71.4
Disorders of carnitine metabolism
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E71.5
Peroxisomal disorders
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E71.11
Branched-chain organic acidurias
Non-billable
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