I42.01
✓ Billable
Familial-genetic dilated cardiomyopathy
ICD-10-CM · FY2026 · Diseases of the Circulatory System
Code
I42.01
System
ICD-10-CM
Billable
Yes — valid for submission
Effective
FY2026
Chapter
Diseases of the Circulatory System
Source
CMS / CDC NCHS
⚠ Verify before billing. Confirm against the current CMS/NCHS ICD-10-CM files and your payer's rules before claims submission.
Official coding notes
From CMS's ICD-10-CM Tabular List.
Includes
- myocardiopathy
Excludes2 — not included here, but may code together
- ischemic cardiomyopathy (I25.5)
- peripartum cardiomyopathy (O90.3)
- ventricular hypertrophy (I51.7)
Code first
- pre-existing cardiomyopathy complicating pregnancy and puerperium (O99.4)
Frequently asked questions
What is ICD-10 code I42.01?
ICD-10-CM code I42.01 represents Familial-genetic dilated cardiomyopathy. It is a billable diagnosis code in the Diseases of the Circulatory System chapter, effective October 1, 2025 – September 30, 2026.
Is I42.01 billable?
Yes. I42.01 is a valid billable ICD-10-CM code for insurance claims and clinical documentation.
What chapter is I42.01 in?
I42.01 belongs to the Diseases of the Circulatory System chapter (I00–I99) of ICD-10-CM.
Related codes in the I42 category
I42
Cardiomyopathy
Non-billable
I42.0
Dilated cardiomyopathy
Non-billable
I42.1
Obstructive hypertrophic cardiomyopathy
Billable
I42.2
Other hypertrophic cardiomyopathy
Billable
I42.3
Endomyocardial (eosinophilic) disease
Billable
I42.4
Endocardial fibroelastosis
Billable
I42.5
Other restrictive cardiomyopathy
Billable
I42.6
Alcoholic cardiomyopathy
Billable
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