M04.3
✓ Billable
VEXAS syndrome
ICD-10-CM · FY2026 · Diseases of the Musculoskeletal System and Connective Tissue
Code
M04.3
System
ICD-10-CM
Billable
Yes — valid for submission
Effective
FY2026
Chapter
Diseases of the Musculoskeletal System and Connective Tissue
Source
CMS / CDC NCHS
⚠ Verify before billing. Confirm against the current CMS/NCHS ICD-10-CM files and your payer's rules before claims submission.
Official coding notes
From CMS's ICD-10-CM Tabular List.
Also known as
- Vacuoles, E1 ubiquitin-activating enzyme, X-linked, autoinflammatory, somatic syndrome
Excludes2 — not included here, but may code together
- Crohn's disease (K50.-)
Code also
- any associated conditions
Frequently asked questions
What is ICD-10 code M04.3?
ICD-10-CM code M04.3 represents VEXAS syndrome. It is a billable diagnosis code in the Diseases of the Musculoskeletal System and Connective Tissue chapter, effective October 1, 2025 – September 30, 2026.
Is M04.3 billable?
Yes. M04.3 is a valid billable ICD-10-CM code for insurance claims and clinical documentation.
What chapter is M04.3 in?
M04.3 belongs to the Diseases of the Musculoskeletal System and Connective Tissue chapter (M00–M99) of ICD-10-CM.
Related codes in the M04 category
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