Q87.A
✓ Billable
Loeys-Dietz syndrome
ICD-10-CM · FY2026 · Congenital Malformations, Deformations and Chromosomal Abnormalities
Code
Q87.A
System
ICD-10-CM
Billable
Yes — valid for submission
Effective
FY2026
Chapter
Congenital Malformations, Deformations and Chromosomal Abnormalities
Source
CMS / CDC NCHS
⚠ Verify before billing. Confirm against the current CMS/NCHS ICD-10-CM files and your payer's rules before claims submission.
Official coding notes
From CMS's ICD-10-CM Tabular List.
Excludes1 — never code together
- arterial tortuosity syndrome (Q87.82)
- Ehlers-Danlos syndrome (Q79.6)
- Marfan syndrome (Q87.40-Q87.43)
- other systemic involvement of connective tissue (M35)
Use additional code
- code(s) to identify all associated manifestations
Frequently asked questions
What is ICD-10 code Q87.A?
ICD-10-CM code Q87.A represents Loeys-Dietz syndrome. It is a billable diagnosis code in the Congenital Malformations, Deformations and Chromosomal Abnormalities chapter, effective October 1, 2025 – September 30, 2026.
Is Q87.A billable?
Yes. Q87.A is a valid billable ICD-10-CM code for insurance claims and clinical documentation.
What chapter is Q87.A in?
Q87.A belongs to the Congenital Malformations, Deformations and Chromosomal Abnormalities chapter (Q00–Q99) of ICD-10-CM.
Related codes in the Q87 category
Q87
Other specified congenital malformation syndromes affecting multiple systems
Non-billable
Q87.0
Congenital malformation syndromes predominantly affecting facial appearance
Billable
Q87.1
Congenital malformation syndromes predominantly associated with short stature
Non-billable
Q87.2
Congenital malformation syndromes predominantly involving limbs
Billable
Q87.3
Congenital malformation syndromes involving early overgrowth
Billable
Q87.4
Marfan syndrome
Non-billable
Q87.5
Other congenital malformation syndromes with other skeletal changes
Billable
Q87.8
Other specified congenital malformation syndromes, not elsewhere classified
Non-billable
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