ICDwise
Q00–Q99

Congenital Malformations, Deformations and Chromosomal Abnormalities

Down syndrome, congenital heart defects

1,086 codes · FY2026 · ICD-10-CM · Page 17 of 22

Q75.03 Metopic craniosynostosis Billable Q75.04 Lambdoid craniosynostosis Non-billable Q75.041 Lambdoid craniosynostosis, unilateral Billable Q75.042 Lambdoid craniosynostosis, bilateral Billable Q75.049 Lambdoid craniosynostosis, unspecified Billable Q75.05 Multi-suture craniosynostosis Non-billable Q75.051 Cloverleaf skull Billable Q75.052 Pansynostosis Billable Q75.058 Other multi-suture craniosynostosis Billable Q75.08 Other single-suture craniosynostosis Billable Q75.1 Craniofacial dysostosis Billable Q75.2 Hypertelorism Billable Q75.3 Macrocephaly Billable Q75.4 Mandibulofacial dysostosis Billable Q75.5 Oculomandibular dysostosis Billable Q75.8 Other specified congenital malformations of skull and face bones Billable Q75.9 Congenital malformation of skull and face bones, unspecified Billable Q76 Congenital malformations of spine and bony thorax Non-billable Q76.0 Spina bifida occulta Billable Q76.1 Klippel-Feil syndrome Billable Q76.2 Congenital spondylolisthesis Billable Q76.3 Congenital scoliosis due to congenital bony malformation Billable Q76.4 Other congenital malformations of spine, not associated with scoliosis Non-billable Q76.41 Congenital kyphosis Non-billable Q76.411 Congenital kyphosis, occipito-atlanto-axial region Billable Q76.412 Congenital kyphosis, cervical region Billable Q76.413 Congenital kyphosis, cervicothoracic region Billable Q76.414 Congenital kyphosis, thoracic region Billable Q76.415 Congenital kyphosis, thoracolumbar region Billable Q76.419 Congenital kyphosis, unspecified region Billable Q76.42 Congenital lordosis Non-billable Q76.425 Congenital lordosis, thoracolumbar region Billable Q76.426 Congenital lordosis, lumbar region Billable Q76.427 Congenital lordosis, lumbosacral region Billable Q76.428 Congenital lordosis, sacral and sacrococcygeal region Billable Q76.429 Congenital lordosis, unspecified region Billable Q76.49 Other congenital malformations of spine, not associated with scoliosis Billable Q76.5 Cervical rib Billable Q76.6 Other congenital malformations of ribs Billable Q76.7 Congenital malformation of sternum Billable Q76.8 Other congenital malformations of bony thorax Billable Q76.9 Congenital malformation of bony thorax, unspecified Billable Q77 Osteochondrodysplasia with defects of growth of tubular bones and spine Non-billable Q77.0 Achondrogenesis Billable Q77.1 Thanatophoric short stature Billable Q77.2 Short rib syndrome Billable Q77.3 Chondrodysplasia punctata Billable Q77.4 Achondroplasia Billable Q77.5 Diastrophic dysplasia Billable Q77.6 Chondroectodermal dysplasia Billable

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