E00–E89
Endocrine, Nutritional and Metabolic Diseases
Diabetes mellitus, obesity, thyroid disorders
E70.33
Albinism with hematologic abnormality
Non-billable
E70.330
Chediak-Higashi syndrome
Billable
E70.331
Hermansky-Pudlak syndrome
Billable
E70.338
Other albinism with hematologic abnormality
Billable
E70.339
Albinism with hematologic abnormality, unspecified
Billable
E70.39
Other specified albinism
Billable
E70.4
Disorders of histidine metabolism
Non-billable
E70.40
Disorders of histidine metabolism, unspecified
Billable
E70.41
Histidinemia
Billable
E70.49
Other disorders of histidine metabolism
Billable
E70.5
Disorders of tryptophan metabolism
Billable
E70.8
Other disorders of aromatic amino-acid metabolism
Non-billable
E70.81
Aromatic L-amino acid decarboxylase deficiency
Billable
E70.89
Other disorders of aromatic amino-acid metabolism
Billable
E70.9
Disorder of aromatic amino-acid metabolism, unspecified
Billable
E71
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
Non-billable
E71.0
Maple-syrup-urine disease
Billable
E71.1
Other disorders of branched-chain amino-acid metabolism
Non-billable
E71.11
Branched-chain organic acidurias
Non-billable
E71.110
Isovaleric acidemia
Billable
E71.111
3-methylglutaconic aciduria
Billable
E71.118
Other branched-chain organic acidurias
Billable
E71.12
Disorders of propionate metabolism
Non-billable
E71.120
Methylmalonic acidemia
Billable
E71.121
Propionic acidemia
Billable
E71.128
Other disorders of propionate metabolism
Billable
E71.19
Other disorders of branched-chain amino-acid metabolism
Billable
E71.2
Disorder of branched-chain amino-acid metabolism, unspecified
Billable
E71.3
Disorders of fatty-acid metabolism
Non-billable
E71.30
Disorder of fatty-acid metabolism, unspecified
Billable
E71.31
Disorders of fatty-acid oxidation
Non-billable
E71.310
Long chain/very long chain acyl CoA dehydrogenase deficiency
Billable
E71.311
Medium chain acyl CoA dehydrogenase deficiency
Billable
E71.312
Short chain acyl CoA dehydrogenase deficiency
Billable
E71.313
Glutaric aciduria type II
Billable
E71.314
Muscle carnitine palmitoyltransferase deficiency
Billable
E71.318
Other disorders of fatty-acid oxidation
Billable
E71.32
Disorders of ketone metabolism
Billable
E71.39
Other disorders of fatty-acid metabolism
Billable
E71.4
Disorders of carnitine metabolism
Non-billable
E71.40
Disorder of carnitine metabolism, unspecified
Billable
E71.41
Primary carnitine deficiency
Billable
E71.42
Carnitine deficiency due to inborn errors of metabolism
Billable
E71.43
Iatrogenic carnitine deficiency
Billable
E71.44
Other secondary carnitine deficiency
Non-billable
E71.440
Ruvalcaba-Myhre-Smith syndrome
Billable
E71.448
Other secondary carnitine deficiency
Billable
E71.5
Peroxisomal disorders
Non-billable
E71.50
Peroxisomal disorder, unspecified
Billable
E71.51
Disorders of peroxisome biogenesis
Non-billable
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