D50–D89
Diseases of the Blood and Blood-Forming Organs
Anemias, coagulation defects, immune disorders
D78.89
Other postprocedural complications of the spleen
Billable
D80
Immunodeficiency with predominantly antibody defects
Non-billable
D80.0
Hereditary hypogammaglobulinemia
Billable
D80.1
Nonfamilial hypogammaglobulinemia
Billable
D80.2
Selective deficiency of immunoglobulin A [IgA]
Billable
D80.3
Selective deficiency of immunoglobulin G [IgG] subclasses
Billable
D80.4
Selective deficiency of immunoglobulin M [IgM]
Billable
D80.5
Immunodeficiency with increased immunoglobulin M [IgM]
Billable
D80.6
Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia
Billable
D80.7
Transient hypogammaglobulinemia of infancy
Billable
D80.8
Other immunodeficiencies with predominantly antibody defects
Billable
D80.9
Immunodeficiency with predominantly antibody defects, unspecified
Billable
D81
Combined immunodeficiencies
Non-billable
D81.0
Severe combined immunodeficiency [SCID] with reticular dysgenesis
Billable
D81.1
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
Billable
D81.2
Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
Billable
D81.3
Adenosine deaminase [ADA] deficiency
Non-billable
D81.30
Adenosine deaminase deficiency, unspecified
Billable
D81.31
Severe combined immunodeficiency due to adenosine deaminase deficiency
Billable
D81.32
Adenosine deaminase 2 deficiency
Billable
D81.39
Other adenosine deaminase deficiency
Billable
D81.4
Nezelof's syndrome
Billable
D81.5
Purine nucleoside phosphorylase [PNP] deficiency
Billable
D81.6
Major histocompatibility complex class I deficiency
Billable
D81.7
Major histocompatibility complex class II deficiency
Billable
D81.8
Other combined immunodeficiencies
Non-billable
D81.81
Biotin-dependent carboxylase deficiency
Non-billable
D81.810
Biotinidase deficiency
Billable
D81.818
Other biotin-dependent carboxylase deficiency
Billable
D81.819
Biotin-dependent carboxylase deficiency, unspecified
Billable
D81.82
Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
Billable
D81.89
Other combined immunodeficiencies
Billable
D81.9
Combined immunodeficiency, unspecified
Billable
D82
Immunodeficiency associated with other major defects
Non-billable
D82.0
Wiskott-Aldrich syndrome
Billable
D82.1
Di George's syndrome
Billable
D82.2
Immunodeficiency with short-limbed stature
Billable
D82.3
Immunodeficiency following hereditary defective response to Epstein-Barr virus
Billable
D82.4
Hyperimmunoglobulin E [IgE] syndrome
Billable
D82.8
Immunodeficiency associated with other specified major defects
Billable
D82.9
Immunodeficiency associated with major defect, unspecified
Billable
D83
Common variable immunodeficiency
Non-billable
D83.0
Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function
Billable
D83.1
Common variable immunodeficiency with predominant immunoregulatory T-cell disorders
Billable
D83.2
Common variable immunodeficiency with autoantibodies to B- or T-cells
Billable
D83.8
Other common variable immunodeficiencies
Billable
D83.9
Common variable immunodeficiency, unspecified
Billable
D84
Other immunodeficiencies
Non-billable
D84.0
Lymphocyte function antigen-1 [LFA-1] defect
Billable
D84.1
Defects in the complement system
Billable
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