ICDwise
D50–D89

Diseases of the Blood and Blood-Forming Organs

Anemias, coagulation defects, immune disorders

401 codes · FY2026 · ICD-10-CM · Page 7 of 9

D78.89 Other postprocedural complications of the spleen Billable D80 Immunodeficiency with predominantly antibody defects Non-billable D80.0 Hereditary hypogammaglobulinemia Billable D80.1 Nonfamilial hypogammaglobulinemia Billable D80.2 Selective deficiency of immunoglobulin A [IgA] Billable D80.3 Selective deficiency of immunoglobulin G [IgG] subclasses Billable D80.4 Selective deficiency of immunoglobulin M [IgM] Billable D80.5 Immunodeficiency with increased immunoglobulin M [IgM] Billable D80.6 Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia Billable D80.7 Transient hypogammaglobulinemia of infancy Billable D80.8 Other immunodeficiencies with predominantly antibody defects Billable D80.9 Immunodeficiency with predominantly antibody defects, unspecified Billable D81 Combined immunodeficiencies Non-billable D81.0 Severe combined immunodeficiency [SCID] with reticular dysgenesis Billable D81.1 Severe combined immunodeficiency [SCID] with low T- and B-cell numbers Billable D81.2 Severe combined immunodeficiency [SCID] with low or normal B-cell numbers Billable D81.3 Adenosine deaminase [ADA] deficiency Non-billable D81.30 Adenosine deaminase deficiency, unspecified Billable D81.31 Severe combined immunodeficiency due to adenosine deaminase deficiency Billable D81.32 Adenosine deaminase 2 deficiency Billable D81.39 Other adenosine deaminase deficiency Billable D81.4 Nezelof's syndrome Billable D81.5 Purine nucleoside phosphorylase [PNP] deficiency Billable D81.6 Major histocompatibility complex class I deficiency Billable D81.7 Major histocompatibility complex class II deficiency Billable D81.8 Other combined immunodeficiencies Non-billable D81.81 Biotin-dependent carboxylase deficiency Non-billable D81.810 Biotinidase deficiency Billable D81.818 Other biotin-dependent carboxylase deficiency Billable D81.819 Biotin-dependent carboxylase deficiency, unspecified Billable D81.82 Activated Phosphoinositide 3-kinase Delta Syndrome [APDS] Billable D81.89 Other combined immunodeficiencies Billable D81.9 Combined immunodeficiency, unspecified Billable D82 Immunodeficiency associated with other major defects Non-billable D82.0 Wiskott-Aldrich syndrome Billable D82.1 Di George's syndrome Billable D82.2 Immunodeficiency with short-limbed stature Billable D82.3 Immunodeficiency following hereditary defective response to Epstein-Barr virus Billable D82.4 Hyperimmunoglobulin E [IgE] syndrome Billable D82.8 Immunodeficiency associated with other specified major defects Billable D82.9 Immunodeficiency associated with major defect, unspecified Billable D83 Common variable immunodeficiency Non-billable D83.0 Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function Billable D83.1 Common variable immunodeficiency with predominant immunoregulatory T-cell disorders Billable D83.2 Common variable immunodeficiency with autoantibodies to B- or T-cells Billable D83.8 Other common variable immunodeficiencies Billable D83.9 Common variable immunodeficiency, unspecified Billable D84 Other immunodeficiencies Non-billable D84.0 Lymphocyte function antigen-1 [LFA-1] defect Billable D84.1 Defects in the complement system Billable

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